Neurofibrosarcoma: case series in south-south Nigeria

  • Authors

    • Maurice Asuquo Department of Surgery, University of Calabar, Calabar
    • Victor Nwagbara Department of Surgery, University of Calabar, Calabar
    • Martin Nnoli Department of Pathology, University of Calabar
    • John Ashindoitiang Department of Surgery, University of Calabar
    • Theophilus Ugbem Department of Pathology, University of Calabar
    • Samuel Akpan Department of Surgery, University of Calabar Teaching Hospital, Calabar
    2017-02-26
    https://doi.org/10.14419/ijm.v5i1.6297
  • Neurofibrosarcoma, Neurofibromatosis -1, Neurofibroma.

  • Abstract

    Neurofibrosarcoma is a malignancy that occurs more frequently in patients with neurofibromatosis- 1 (NF- 1) and rarely may arise independently. This is a presentation of 3 consecutive patients with histologic diagnosis of neurofibrosarcoma who presented to the University of Calabar Teaching Hospital, Calabar from 2011-2013. Two patients presented were associated with NF-1 and were a decade younger than the one without NF-1. Late presentation and poor follow up were notable underlying factors. Long term follow up of patients with NF -1 for early diagnosis and adequate treatment will improve outcome.

  • References

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  • How to Cite

    Asuquo, M., Nwagbara, V., Nnoli, M., Ashindoitiang, J., Ugbem, T., & Akpan, S. (2017). Neurofibrosarcoma: case series in south-south Nigeria. International Journal of Medicine, 5(1), 79-81. https://doi.org/10.14419/ijm.v5i1.6297

    Received date: 2016-05-23

    Accepted date: 2016-07-09

    Published date: 2017-02-26